 |
|
Kearns-Sayre SyndromeA Review of a Multisystem Disorder of Children and Young Adults
Ian J. Butler, MB, BS, FRACP;
Natan Gadoth, MD
Arch Intern Med. 1976;136(11):1290-1293.
Abstract
The syndrome of a slowly progressive external ophthalmoplegia, pigment retinopathy, and disorder of cardiac conduction was described by Kearns and Sayre in 1958. In patients with this triad, other neurological deficits may occur with associated abnormalities of the electrocardiogram, electroencephalogram, audiogram, and an elevation of protein in cerebrospinal fluid. The onset of a potentially lethal cardiac dysrhythmia in a patient with this slowly progressive degeneration of the nervous system can be anticipated and prevented by the use of an artificial cardiac pacemaker.
(Arch Intern Med 136:1290-1293, 1976)
Author Affiliations
From the Department of Neurology, Johns Hopkins University School of Medicine, Baltimore.
Footnotes
Received for publication July 21, 1975; accepted Jan 20, 1976.
Reprint requests to Department of Neurology, University of Texas Medical School at Houston, 6301 Almeda, Houston, TX 77021 (Dr Butler).
 CiteULike  Connotea  Del.icio.us  Digg  Reddit  Technorati  Twitter
What's this?
THIS ARTICLE HAS BEEN CITED BY OTHER ARTICLES
Chronic progressive ophthalmoplegia with large-scale mtDNA rearrangement: can we predict progression?
Aure et al.
Brain 2007;130:1516-1524.
ABSTRACT
| FULL TEXT
Myocardial Ultrastructure in Kearns-Sayre Syndrome
Nakano et al.
ANGIOLOGY 1987;38:28-35.
ABSTRACT
Near-fatal Kearns-Sayre Syndrome: A Case Report and Review of Clinical Manifestations
Rheuban et al.
CLIN PEDIATR 1983;22:822-825.
ABSTRACT
Abrupt Neurological Deterioration in Children With Kearns-Sayre Syndrome
Coulter and Allen
Arch Neurol 1981;38:247-250.
ABSTRACT
|
