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J. Aidan Carney, MD, PhD, FRCPI

Arch Intern Med. 1987;147(3):418-419.

	Since this article does not have an abstract, we have provided the first 150 words of the full text PDF and any section headings.

The syndrome discussed by Danoff and associates¹ in this issue of the ARCHIVES is a newly recognized condition¹ that was "synthesized" from some personal observations, along with bits and pieces and good-sized chunks of information gleaned from the literature. The complex includes myxomas (cardiac, cutaneous, and mammary), spotty mucocutaneous pigmentation, and endocrine overactivity (Cushing's syndrome, sexual precocity, and acromegaly or gigantism). Most of the constituents of the complex are probably now known, but there are still some candidate components—such as uterine myxoma, acoustic neuroma, taillike appendage, thyroid neoplasms, and fibrolamellar hepatoma—that have occurred singly in affected patients (tumors in the complex are usually multicentric).

Among the 40 patients included in our article on the complex² were two genetically unrelated patients who, in addition to other components of the syndrome, had a peculiar pigmented neural tumor with features of schwannoma. Although the neoplasm was single in both, we suggested that it . . . [Full Text PDF of this Article]

Author Affiliations
Mayo Clinic and Mayo Foundation Rochester, MN 55905

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